From: Phenotypes and outcome of diffuse pulmonary non-amyloid light chain deposition disease
Feature | n (%) |
---|---|
Cysts | 26 (100%) |
Shape | |
Oval | 2 (8%) |
Irregular | 3 (11%) |
Round | 6 (23%) |
No predominance | 15 (58%) |
Internal septation | 19 (73%) |
Peribronchovascular | 20 (77%) |
Vertical distribution | |
Upper predominance | 3 (11.5%) |
Middle predominance | 3 (11.5%) |
Lower predominance | 14(54%) |
No predominance | 6 (23% |
Axial distribution | |
No predominance | 17 (70%) |
Central | 6 (23%) |
Peripheral | 3 (12%) |
Number | |
< 50 | 7 (27%) |
50–100 | 6 (23%) |
> 100 | 13 (50%) |
Location of largest cysts | |
Abutting the pleura | 21 (80%) |
Surrounded by lung parenchyma | 5 (20%) |
Bronchiectasis | 20 (77%) |
Shape | |
Cystic | 1 (5%) |
Cylindric | 0 |
Varicose | 19 (95%) |
Vertical Distribution | |
No predominance | 10 (56%) |
Upper predominance | 0 |
Lower predominance | 8 (44%) |
Horizontal distribution | |
Proximal predominance | 1 (5%) |
Distal predominance | 19 (95%) |
Bronchial wall | |
Normal | 3 (12%) |
Thin | 17 (65%) |
Thick | 6 (23%) |
Bronchocele, mucus plug | 9 (37%) |
Predominant imaging pattern | |
Cystic | 15 (58%) |
Bronchiectasis | 7 (27%) |
Mixed | 4 (15%) |
Nodules (< 1 cm in diameter) | 11 (42%) |
Lymphadenopathy | |
Supracentimetric mediastinal lymph node | 4 (15%) |
Infracentimetric mediastinal lymph node | 16 (61%) |
Hilar lymph node | 9 (37%) |
Consolidation | 5 (19%) |
Emphysema | 9 (35%) |