Table 1 Patient characteristics

Number

18

19

Age

54 (46–63)

65 (62–67)

0.001

Sex: male

6 (33%)

18 (95%)

0.001

RP-ILD or IPF-AE

9 (50%)

9 (47%)

Tissue collection method

 SLB

11 (61%)

10 (53%)

 Transplant

1 (6%)

0 (0%)

 Autopsy

6 (33%)

9 (47%)

Dx of IIMs

 DM

12 (67%)

–

 CADM

6 (33%)

–

Histological pattern

 DAD

11 (61%)

9 (47%)

 NSIP

6 (33%)

0 (0%)

 UIP

1 (6%)

10 (53%)

Treatment for autopsy and lung transplant cases

 Corticosteroid

7 (100%)

8 (89%)

 Calcineurin inhibitors

6 (86%)

2 (22%)

 Cyclophosphamide

5 (71%)

3 (33%)

Cause of death in autopsy cases

 Respiratory failure (including IPF-AE or RP-ILD)

6 (100%)

6 (67%)

 Lung cancer

0 (0%)

3 (33%)