From: A proposed prognostic prediction score for pleuroparenchymal fibroelastosis
Predictor | GAP score | PPFE prognosis score |
---|---|---|
Gender | female (0), male (1) | – |
Age, year | ≤ 60 (0), 61–65 (1), > 65 (2) | – |
FVC, % predicted | > 75 (0), 50–75 (1), < 50 (2) | ≥ 65 (0), < 65 (1) |
DLCO, % predicted | > 55 (0), 36–55 (1), ≤ 35 (2), cannot perform (3) | – |
History of pneumothorax | – | No (0), yes (1) |
ILD in the lower lobes* | – | No (0), yes (1) |
KL-6, U/ml | – | ≤ 550 (0), > 550 (1) |
Total points | I (0–3), II (4–5), III (6–8) | I (0–1), II (2), III (3–4) |