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Table 6 The comparison between GAP score and PPFE prognosis score

From: A proposed prognostic prediction score for pleuroparenchymal fibroelastosis

Predictor

GAP score

PPFE prognosis score

Gender

female (0), male (1)

–

Age, year

≤ 60 (0), 61–65 (1), > 65 (2)

–

FVC, % predicted

> 75 (0), 50–75 (1), < 50 (2)

≥ 65 (0), < 65 (1)

DLCO, % predicted

> 55 (0), 36–55 (1), ≤ 35 (2), cannot perform (3)

–

History of pneumothorax

–

No (0), yes (1)

ILD in the lower lobes*

–

No (0), yes (1)

KL-6, U/ml

–

≤ 550 (0), > 550 (1)

Total points

I (0–3), II (4–5), III (6–8)

I (0–1), II (2), III (3–4)

  1. The figures in parentheses indicate the corresponding points
  2. GAP gender-age-physiology, FVC forced vital capacity, DLCO diffusing capacity of the lung for carbon monoxide, ILD interstitial lung disease, KL-6 Krebs von den Lungen-6
  3. *ILD in the lower lobes indicates any pattern of fibrosis including the UIP pattern and PPFE