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Table 1 List of some of the rare lung disorders

From: Educational aspects of rare and orphan lung diseases

Rare lung disease

α1-antitrypsin deficiency

Cystic fibrosis (CF)

Non-CF bronchiectasis

Primary ciliary dyskinesia (PCD)

Interstitial lung diseases (ILD)

 Idiopathic pulmonary fibrosis (IPF)

 Sarcoidosis

 Connective tissue diseases

 Lymphangioleiomyomatosis (LAM)

 Birt–Hogg–Dubé syndrome

 Eosinophilic pneumonia

 Pulmonary alveolar proteinosis

 Adult pulmonary Langerhans cell histiocytosis

 Granulomatous lymphocytic interstitial lung disease (GLILD)

 Other interstitial lung diseases

Pulmonary hypertension

 Pulmonary arterial hypertension

 Chronic thromboembolic pulmonary hypertension

Chronic lung allograft dysfunction

 Bronchiolitis obliterans syndrome (BOS)

 Restrictive allograft syndrome (RAS)

Mesothelioma

Other rare lung diseases