Controls | HHT | PAVMs | P + LAVMs | LAVMs | |
---|---|---|---|---|---|
n | 15 | 7 | 8 | 25 | 21 |
Age, yr. a | 46 (23;53) | 27 (18;59) | 40 (35;51.75) | 36 (29;47) | 43.7 (32.5;55.5) |
Female/Male ratio a | 10/5 | 2/5 | 4/4 | 16/9 | 17/4 |
LVEF,% a | nd | 69 (61;73) | 63 (61.5;71.75) | 70 (67;76) | 71 (68.5;75.5) |
(A-a) O2 a (kPa) | nd | 1.25 (0;2.92) | 2 (1.5;2.85) | 2 (0.5;3.7) | 1.15 (0.5;1.75) |
Hb, g/dL a | nd | 14.9 (14.5;15.1) | 14.55 (13.8;15.2) | 14.2 (13.5;15) | 14 (12.1;14.7) |
TLC, % a | 93.8 (90;100) | 99 (90;102) | 104.5 (99.25;113) | 104 (94.5;111.5) | 101 (91;117.5) |
DLCO,% a | 88.5 (85;92.8) | 85 (80;97) | 104 (91.75;110) | 81 (74.5;86.5) | 91 (79.5;98.5) |
DLCO/VA,% a | 95.2 (90.6;112.9) | 98 (92.5;102.5) | 100 (78;111) | 88 (81;95) | 94 (86.25;104) |
DLNO/DLCO | 4.1 (3.8;4.3) | 4.5 (4.3;4.7)# | 4.3 (4.2;4.6) | 4.5 (4.25;4.6)# | 4.3 (3.95;4.5) |
Vc, % a | 85 (76.7;91.9) | 85 (79;93) | 103.5 (94.25;110.8) | 78 (73;89) | 94 (79;97) |
Dm, % a | 125.5 (120.7;139.2) | 113 (102;119) | 135.5 (129.3;147.3) | 107 (98.5;116) | 117 (100;125.5) |
Vc/Dm ratio | 1.09 (1.01;1.2) | 1.15 (1.13;1.25) | 1.21 (1.12;1.26) | 1.16 (1.11;1.42) | 1.35 (1.18;1.62)b |