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Table 1 Baseline characteristics

From: Birt-Hogg-Dubé syndrome: a large single family cohort

Characteristic Value
Age at Diagnosis, yrs 42 (3.1)
Male:Female 18:18
BMI, kg/m2 25.7 (0.85)
Smokers, n (%)  
 Current 3 (9)
 Former 4 (11)
 Never 17 (47)
 Unknown status 12 (33)
Smoking, pack years 6.9 (3.05)
FEV1, L 3.32 (0.21)
FEV1 (% pred) 92 (3.64)
FVC, L 4.40 (0.27)
FVC (% pred) 101 (4.10)
FEV1/FVC 74.8 (2.07)
DLCO, mL/min/mmHg 33.32 (2.26)
DLCO (% pred) 130 (6.72)
DLCO/VA, mL/min/mmHg 27.1 (3.66)
DLCO/VA (% pred) 130 (5.67)
DLCO, mL/min/mmHg (Asthmatics excluded) 33.0 (2.56)
DLCO (% pred) (Asthmatics excluded) 133.9 (7.40)
Asthma diagnosis, n (%) 6 (17)
  1. Asthma was defined as full reversibility of airflow obstruction following bronchodilator administration or a positive methacholine challenge test. Data are shown as mean (SD)
  2. Abbreviations: BMI body mass index, DL CO diffusing capacity for carbon monoxide, FEV1 forced expiratory volume in one second, FRC functional residual capacity, FVC forced vital capacity