| 100 SSc patients |
---|---|
FVC % mean ± sd | 100.1 ± 22.1 |
≤ 79% n (%) | 16 (16.0%) |
≤ 69% n (%) | 12 (12.0%) |
≤ 49% n (%) | 1 (1.0%) |
DLCO % mean ± sd | 59.4 ± 17.3 |
≤ 79% n (%) | 90 (90.0%) |
≤ 69% n (%) | 83 (83.0%) |
≤ 49% n (%) | 29 (29.0%) |
PASP ≥ 40 mmHg n (%)* | 11 (11.8%)* |
≥ 60 mmHg n (%)* | 2 (2.2%)* |
HRCT: interstitial score ≥ 2, n (%)* | 87 (93.5%)* |
mean total score ± sd | 3.1 ± 4.2 |
HRCT: alveolar score ≥ 2, n (%)* | 55 (59.1%)* |
mean total score ± sd | 5.7 ± 2.6 |
BAL: alveolitis n (%)** | 16 (38.1%)** |
N ≥ 5 % n (%)** | 11 (68.8%)** |
N ≥ 5 % and L ≥ 15 % n (%)** | 2 (12.5%)** |
N ≥ 5 % and E ≥ 5 % n (%)** | 2 (12.5%)** |
N ≥ 5 %, L ≥ 15 % and E ≥ 5 % n (%)** | 1 (6.2%)** |
N < 5 % and L ≥ 15 % and/or E ≥ 5 % n (%)** | 0 (0.0%)** |
BAL with positive cultures n (%)** | 10 (23.8%)** |