Subjects, n | 51 |
Sex (F/M) | 14/37 |
Age, years | 31 ± 14 |
Children (< 18 years)/Adults | 9/42 |
F508del/F508del (yes/no) | 25/26 |
Sweat Chloride, mmol/L | 106 (29; 140) |
Pancreatic sufficiency (yes/no) | 14/37 |
Pseudomonas aeruginosa chronic infection (yes/no) | 19/32 |
Diabetes (yes/no) | 9/42 |
Smokers (yes/no) | 4/47 |
BMI, kg/m2 | 21.05 (14.65; 33.80) |
FEV1, L | 2.69 ± 1.17 |
FEV1, %PV | 74.21 ± 22.37 |
1STST, n | 34 (17; 68) |
1STST, %PV [26] | 79 (7; 142) |
1STST, nxkg | 2101 ± 657 |
MVCQ, N-m | 78.64 (23.21; 170.34) |
MVCQ, %PV [28] | 56.73 ± 26.21 |