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Table 2 Site-specific event rates of outcomes at 1 year

From: Associations between resources and practices of ILD centers and outcomes in patients with idiopathic pulmonary fibrosis: data from the IPF-PRO Registry

 

Median (Q1, Q3) 1-year event ratea, %

Death or lung transplant

9.8 (6.3, 17.5)

Hospitalization

21.3 (12.5, 30.8)

Decline in FVC ≥ 10% (mL) or death or lung transplant

32.0 (21.4, 37.5)

Decline in FVC ≥ 10% predicted or death or lung transplant

21.4 (13.9, 28.5)

Decline in DLco ≥ 15% (mmol/min/kPa) or death or lung transplant

35.1 (26.7, 45.7)

Decline in DLco ≥ 15% predicted or death or lung transplant

15.1 (11.1, 25.0)

Increase in SGRQ total score ≥ 7 or death or lung transplant

35.3 (29.8, 43.6)

Increase in SGRQ activity score ≥ 5 or death or lung transplant

48.6 (39.2, 57.5)

Increase in SGRQ impact score ≥ 7 or death or lung transplant

34.8 (30.6, 43.5)

Increase in SGRQ symptoms score ≥ 8 or death or lung transplant

35.7 (25.8, 42.5)

Decrease in CASA-Q cough impact domain ≥ 11 or death or lung transplant

32.3 (26.3, 39.7)

Decrease in CASA-Q cough symptoms domain ≥ 11 or death or lung transplant

31.4 (25.9, 36.3)

Decrease in EuroQoL-5D index score ≥ 0.06 or death or lung transplant

37.7 (28.6, 43.8)

Decrease in EuroQoL-5D VAS score ≥ 8 or death or lung transplant

38.7 (29.5, 45.8)

Decrease in SF-12 MCS score ≥ 6 or death or lung transplant

28.7 (24.0, 33.5)

Decrease in SF-12 PCS score ≥ 5 or death or lung transplant

33.5 (30.3, 40.2)

  1. CASA-Q cough and sputum assessment questionnaire, DLco diffusing capacity of the lungs for carbon monoxide, FVC forced vital capacity, MCS mental component summary, PCS physical component summary, SF-12 12-item short-form survey, SGRQ St. George’s Respiratory Questionnaire, VAS visual analog scale
  2. aCumulative incidence rate for hospitalization; Kaplan–Meier rates reported for all other outcomes