From: A proposed prognostic prediction score for pleuroparenchymal fibroelastosis
Variables | Classification | Points |
---|---|---|
%FVC (< 65%) | Yes | 1 |
No | 0 | |
History of pneumothorax | Yes | 1 |
No | 0 | |
ILD in the lower lobes* | Yes | 1 |
No | 0 | |
KL-6 (> 550U/ml) | Yes | 1 |
No | 0 | |
Stage | Grade | Â |
 | I | 0–1 |
 | II | 2 |
 | III | 3–4 |