From: Global incidence and prevalence of idiopathic pulmonary fibrosis
Country | Study | Publication year | Mean unadjusted prevalence (per 10,000) | Adjusted prevalence (per 10,000) | 95% CI Adjusted prevalence (per 10,000) | Rare disease threshold (per 10,000) | Rare disease threshold met? |
---|---|---|---|---|---|---|---|
Asia–Pacific | |||||||
 Taiwan | Lai et al. [43] | 2012 | 0.64 | 0.79 | (0.36, 1.74) | 1 [27] | Yes (upper CI out of bounds) |
Europe | |||||||
 Italy | Agabiti et al. [33] | 2014 | 2.56 | 3.08 | (1.11, 8.55) | 5 [29] | Yes (upper CI out of bounds) |
Harari et al. [37] | 2016 | 3.61 | |||||
Combined | Â | 3.27 | |||||
 United Kingdom | Snell et al. [49] | 2016 | 5.00 | 4.06 | (1.98, 8.33) | 5 [29] | Yes (upper CI out of bounds) |
Strongman et al. [13] | 2018 | 3.88 | |||||
Combined | Â | 4.16 | |||||
North America | |||||||
 Canada | Hopkins et al. [38] | 2016 | 4.18 | 3.99 | (1.73, 9.23) | 5 [30] | Yes (upper CI out of bounds) |
Tarride et al. [12] | 2018 | 7.84 | |||||
Combined | Â | 4.86 | |||||
 United States | Esposito et al. [36] | 2015 | 12.52 | 5.67 | (1.74, 18.47) | < 200,000a [31] | Yes (upper CI out of bounds) |
Fernández Pérez et al. [11] | 2010 | 6.30 | |||||
Raghu et al. [47] | 2014 | 18.1 | |||||
Raghu et al. [46] | 2016 | 0.49 | |||||
Raimundo et al. [48] | 2016 | 1.98 | |||||
Combined | Â | 2.96 |