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Table 3 IPF prevalence estimates utilizing broad case definitions per country

From: Global incidence and prevalence of idiopathic pulmonary fibrosis

Country

Study

Publication year

Mean unadjusted prevalence (per 10,000)

Adjusted prevalence (per 10,000)

95% CI Adjusted prevalence (per 10,000)

Rare disease threshold (per 10,000)

Rare disease threshold met?

Asia–Pacific

 Taiwan

Lai et al. [43]

2012

0.64

0.79

(0.36, 1.74)

1 [27]

Yes (upper CI out of bounds)

Europe

 Italy

Agabiti et al. [33]

2014

2.56

3.08

(1.11, 8.55)

5 [29]

Yes (upper CI out of bounds)

Harari et al. [37]

2016

3.61

Combined

 

3.27

 United Kingdom

Snell et al. [49]

2016

5.00

4.06

(1.98, 8.33)

5 [29]

Yes (upper CI out of bounds)

Strongman et al. [13]

2018

3.88

Combined

 

4.16

North America

 Canada

Hopkins et al. [38]

2016

4.18

3.99

(1.73, 9.23)

5 [30]

Yes (upper CI out of bounds)

Tarride et al. [12]

2018

7.84

Combined

 

4.86

 United States

Esposito et al. [36]

2015

12.52

5.67

(1.74, 18.47)

< 200,000a [31]

Yes (upper CI out of bounds)

Fernández Pérez et al. [11]

2010

6.30

Raghu et al. [47]

2014

18.1

Raghu et al. [46]

2016

0.49

Raimundo et al. [48]

2016

1.98

Combined

 

2.96

  1. CI confidence interval, IPF idiopathic pulmonary fibrosis
  2. aNumber of cases provided rather than threshold