Fig. 1

Prevalence of PH in PF patients. Graphical representation of the prevalence of PH found in the PF patient population in multiple studies. Studies in black used right heart catheterization (RHC) with a mean Pulmonary Arterial Pressure (mPAP) above 25 mmHg to define PH. Studies in blue used transthoracic echography (TTE) to define PH with a calculated systolic pulmonary arterial pressure (SPAP) above 35 mmHg except Song et al. which used a SPAP above 40 mmHg to define PH. PLCH (Pulmonary Langerhans Cell Histiocytosis); CHP (Chronic Hypersensitivity Pneumonitis); Ssc (Systemic Scleroderma); IPF (Idiopathic Pulmonary Fibrosis)