Baseline | Post-Treatment | |
---|---|---|
Male:Female | 3:4 | |
Age, years | 29 (10) | 30 (9) |
Height, cm | 164 (9) | 164 (9) |
Mass, kg | 59.3 (9.5) | 60.3 (9.1) |
BMI, kg/m2 | 20.2 (3.1) | 20.5 (3.0)* |
SGRQ, total score | 37.1 (17.8) | 26.3 (16.9) |
IPAQ-LF, MET-min/week | 2910 (1676) | 1754 (3322) |
Sweat Chloride, mmol/L | 103 (25) | 90 (18)* |
Pulmonary Function | ||
FEV1, L | 1.44 (0.22) | 1.45 (0.45) |
FEV1, %pred | 46 (18) | 49 (19) |
FVC, L | 3.17 (0.49) | 3.11 (0.57) |
FVC, %pred | 73 (21) | 69 (28) |
FEV1/FVC, % | 49.1 (10.8) | 54.3 (10.3) |
TLC, L | 6.17 (1.91) | 5.93 (2.10) |
TLC, %pred | 97 (17) | 100 (27) |
DLCO, mL/mmHg/min | 17.4 (6.5) | 18.9 (6.6) |
DLCO, %pred | 78 (22) | 90 (18) |