Variable | Lobectomised PCD (n = 130) Median (IQR) | iPCD Cohort (n = 2733)a Median (IQR) | p-value | |
---|---|---|---|---|
Age at Presentation (n = 118) | 11.5 (6.5, 20.5) | 8.8 (4.0, 15.8) | < 0.001† | |
Current Age (n = 130) | 24.9 (18.1, 40.1) | 18.6 (12.1, 28.3) | < 0.001† | |
% Female | 72/130 (55.4%) | 1302/2661 (48.9%) | 0.150‡ | |
Situs Inversus | 27/108 (25.0%) | 787/1783 (44.1%) | < 0.001‡ | |
Age at lung resection (n = 121) | 11.9 (7.7, 16.0) | |||
Lung resection prior to presentation | 52/114 (45.6%) | |||
Lung resection in childhood | 101/121 (83.5%) | |||
Frequency of lung resection performance per decade (n = 121) | < 1969 | 4 | < 0.001‡ | |
1970–1979 | 11 | |||
1980–1989 | 9 | |||
1990–1999 | 24 | |||
2000–2009 | 34 | |||
2010–2017 | 39 | |||
Extent of lung resection (n = 95) | One Lobe: 74/95 | |||
(77.9%) | ||||
Two lobes: 17/95 | ||||
(17.9%) | ||||
Three Lobes: 2/95 | ||||
(2.1%) | ||||
Four Lobes: 2/95 | ||||
(2.1%) | ||||
Site of lung resectionb (n = 95) | RML: 59/121 (48.8%) | |||
LLL: 33/121 (27.3%) | ||||
RLL: 13/121 (10.7%) | ||||
Lingula: 9/121 (7.4%) | ||||
RUL: 5/121 (4.1%) | ||||
LUL: 2/121 (1.7%) |