Fig. 2

QoL at last follow-up visit and Change in QoL from baseline to last follow-up visit by change in lung function. * p-value < 0.05 in comparison to category ‘stable/ increase’ DLCO % predicted: diffusing capacity of the lung for carbon monoxide % predicted; FVC % predicted, forced vital capacity % predicted; QoL, quality of life; SGRQ, St. George’s Respiratory Questionnaire