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Table 1 Clinical features (n = 33)

From: Immunohistological features related to functional impairment in lymphangioleiomyomatosis

Age at pulmonary biopsy or transplantation, years

42 ± 8

Age at diagnosis, years

40 ± 8

Presence of TSC

3 (9%)

Renal angiomyolipoma

15 (46%)

Ex-smokers

7 (21%)

Dyspnea

23 (70%)

Baseline dyspnea index

10 (8 - 12)

Pneumothorax

22 (67%)

Hemoptysis

5 (15%)

Cough

4 (12%)

Chylothorax

3 (9%)

Supplemental oxygen

6 (18%)

  1. Values are the mean ± SD, median (interquartile range) or percentage (%)
  2. TSC tuberous sclerosis complex