From: Genetic analyses in a cohort of 191 pulmonary arterial hypertension patients
Characteristic | IPAH (n = 179) | HPAH (n = 12) |
---|---|---|
Age at diagnosis, y | 30.7 ± 10.6 | 24.8 ± 7.2 |
Female sex | 135 (75.4%) | 7 (58.3%) |
NYHA I-II | 82 (45.8%) | 6 (50.0%) |
NYHA III | 91 (50.8%) | 5 (41.7%) |
NYHA IV | 6 (3.4%) | 1 (8.3%) |
Hemodynamics at diagnosis | ||
RAP, mmHg | 5.2 ± 4.2 | 2.8 ± 4.5 |
mPAP, mmHg | 56.1 ± 14.7 | 61.6 ± 16.4 |
PVR, dyn*s*cm− 5 | 1155.6 ± 523.6 | 1052.8 ± 422.4 |
PAWP, mmHg | 7.1 ± 3.5 | 7.1 ± 3.1 |
CI, L/min/m2 | 2.8 ± 0.9 | 3.1 ± 1.2 |
SvO2, % | 67.8 ± 7.5 | 71.4 ± 6.3 |
Peak VO2, ml/min/Kg | 13.1 ± 3.6 | 12.2 ± 2.2 |
6-min walk distance, m | 415.6 ± 101.3 | 435.5 ± 100.3 |
NT-proBNP, pg/ml | 1403.6 ± 1327.4 | 970.1 ± 881.8 |