TY - JOUR AU - Kerem, E. AU - Reisman, J. AU - Corey, M. AU - Canny, G. J. AU - Levison, H. PY - 1992 DA - 1992// TI - Prediction of mortality in patients with cystic fibrosis JO - N Engl J Med VL - 326 UR - https://doi.org/10.1056/NEJM199204303261804 DO - 10.1056/NEJM199204303261804 ID - Kerem1992 ER - TY - JOUR AU - Farrell, P. M. AU - Rosenstein, B. J. AU - White, T. B. AU - Accurso, F. J. AU - Castellani, C. AU - Cutting, G. R. AU - Durie, P. R. AU - LeGrys, V. A. AU - Massie, J. AU - Parad, R. B. PY - 2008 DA - 2008// TI - Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report JO - J Pediatr VL - 153 UR - https://doi.org/10.1016/j.jpeds.2008.05.005 DO - 10.1016/j.jpeds.2008.05.005 ID - Farrell2008 ER - TY - JOUR AU - Milla, C. E. AU - Warwick, W. J. PY - 1998 DA - 1998// TI - Risk of death in cystic fibrosis patients with severely compromised lung function JO - Chest VL - 113 UR - https://doi.org/10.1378/chest.113.5.1230 DO - 10.1378/chest.113.5.1230 ID - Milla1998 ER - TY - JOUR AU - Flume, P. A. AU - Mogayzel, P. J. AU - Robinson, K. A. AU - Goss, C. H. AU - Rosenblatt, R. L. AU - Kuhn, R. J. AU - Marshall, B. C. PY - 2009 DA - 2009// TI - Cystic fibrosis pulmonary guidelines: treatment of pulmonary exacerbations JO - Am J Respir Crit Care Med VL - 180 UR - https://doi.org/10.1164/rccm.200812-1845PP DO - 10.1164/rccm.200812-1845PP ID - Flume2009 ER - TY - JOUR AU - Liou, T. G. AU - Adler, F. R. AU - FitzSimmons, S. C. AU - Cahill, B. C. AU - Hibbs, J. R. AU - Marshall, B. C. PY - 2001 DA - 2001// TI - Predictive 5-year survivorship model of cystic fibrosis JO - Am J Epidemiol VL - 153 UR - https://doi.org/10.1093/aje/153.4.345 DO - 10.1093/aje/153.4.345 ID - Liou2001 ER - TY - JOUR AU - Courtney, J. AU - Bradley, J. AU - Mccaughan, J. AU - O’connor, T. AU - Shortt, C. AU - Bredin, C. AU - Bradbury, I. AU - Elborn, J. PY - 2007 DA - 2007// TI - Predictors of mortality in adults with cystic fibrosis JO - Pediatr Pulmonol VL - 42 UR - https://doi.org/10.1002/ppul.20619 DO - 10.1002/ppul.20619 ID - Courtney2007 ER - TY - JOUR AU - Puchelle, E. AU - Gaillard, D. AU - Ploton, D. AU - Hinnrasky, J. AU - Fuchey, C. AU - Boutterin, M. C. AU - Jacquot, J. AU - Dreyer, D. AU - Pavirani, A. AU - Dalemans, W. PY - 1992 DA - 1992// TI - Differential localization of the cystic fibrosis transmembrane conductance regulator in normal and cystic fibrosis airway epithelium JO - Am J Respir Cell Mol Biol VL - 7 UR - https://doi.org/10.1165/ajrcmb/7.5.485 DO - 10.1165/ajrcmb/7.5.485 ID - Puchelle1992 ER - TY - JOUR AU - Baker, S. E. AU - Wong, E. C. AU - Wheatley, C. M. AU - Foxx-Lupo, W. T. AU - Martinez, M. G. AU - Morgan, M. A. AU - Sprissler, R. AU - Morgan, W. J. AU - Snyder, E. M. PY - 2012 DA - 2012// TI - Genetic variation of SCNN1A influences lung diffusing capacity in cystic fibrosis JO - Med Sci Sports Exerc VL - 44 UR - https://doi.org/10.1249/MSS.0b013e318266ebc3 DO - 10.1249/MSS.0b013e318266ebc3 ID - Baker2012 ER - TY - JOUR AU - Wheatley, C. M. AU - Foxx-Lupo, W. T. AU - Cassuto, N. A. AU - Wong, E. C. AU - Daines, C. L. AU - Morgan, W. J. AU - Snyder, E. M. PY - 2011 DA - 2011// TI - Impaired lung diffusing capacity for nitric oxide and alveolar-capillary membrane conductance results in oxygen desaturation during exercise in patients with cystic fibrosis JO - J Cyst Fibros VL - 10 UR - https://doi.org/10.1016/j.jcf.2010.09.006 DO - 10.1016/j.jcf.2010.09.006 ID - Wheatley2011 ER - TY - JOUR AU - Dalemans, W. AU - Barbry, P. AU - Champigny, G. AU - Jallat, S. AU - Dott, K. AU - Dreyer, D. AU - Crystal, R. G. AU - Pavirani, A. AU - Lecocq, J. P. AU - Lazdunski, M. PY - 1991 DA - 1991// TI - Altered chloride ion channel kinetics associated with the delta F508 cystic fibrosis mutation JO - Nature VL - 354 UR - https://doi.org/10.1038/354526a0 DO - 10.1038/354526a0 ID - Dalemans1991 ER - TY - JOUR AU - Lands, L. C. AU - Heigenhauser, G. J. AU - Jones, N. L. PY - 1992 DA - 1992// TI - Cardiac output determination during progressive exercise in cystic fibrosis JO - Chest VL - 102 UR - https://doi.org/10.1378/chest.102.4.1118 DO - 10.1378/chest.102.4.1118 ID - Lands1992 ER - TY - JOUR AU - Nixon, P. A. AU - Orenstein, D. M. AU - Kelsey, S. F. AU - Doershuk, C. F. PY - 1992 DA - 1992// TI - The prognostic value of exercise testing in patients with cystic fibrosis JO - N Engl J Med VL - 327 UR - https://doi.org/10.1056/NEJM199212173272504 DO - 10.1056/NEJM199212173272504 ID - Nixon1992 ER - TY - JOUR AU - Hart, M. A. AU - Konstan, M. W. AU - Darrah, R. J. AU - Schluchter, M. D. AU - Storfer-Isser, A. AU - Xue, L. AU - Londono, D. AU - Goddard, K. A. AU - Drumm, M. L. PY - 2005 DA - 2005// TI - Beta 2 adrenergic receptor polymorphisms in cystic fibrosis JO - Pediatr Pulmonol VL - 39 UR - https://doi.org/10.1002/ppul.20210 DO - 10.1002/ppul.20210 ID - Hart2005 ER - TY - JOUR AU - Marson, F. A. L. AU - Bertuzzo, C. S. AU - Ribeiro, A. F. AU - Ribeiro, J. D. PY - 2012 DA - 2012// TI - Polymorphisms in ADRB2 gene can modulate the response to bronchodilators and the severity of cystic fibrosis JO - BMC Pulmonary Med VL - 12 UR - https://doi.org/10.1186/1471-2466-12-50 DO - 10.1186/1471-2466-12-50 ID - Marson2012 ER - TY - JOUR AU - Shapiro, G. G. AU - Bamman, J. AU - Kanarek, P. AU - Bierman, C. W. PY - 1976 DA - 1976// TI - The paradoxical effect of adrenergic and methylxanthine drugs in cystic fibrosis JO - Pediatrics VL - 58 ID - Shapiro1976 ER - TY - JOUR AU - Featherby, E. A. AU - Weng, T. R. AU - Levison, H. PY - 1970 DA - 1970// TI - The effect of isoproterenol on airway obstruction in cystic fibrosis JO - Can Med Assoc J VL - 102 ID - Featherby1970 ER - TY - JOUR AU - Larsen, G. L. AU - Barron, R. J. AU - Cotton, E. K. AU - Brooks, J. G. PY - 1979 DA - 1979// TI - A comparative study of inhaled atropine sulfate and isoproterenol hydrochloride in cystic fibrosis JO - Am Rev Respir Dis VL - 119 ID - Larsen1979 ER - TY - JOUR AU - Büscher, R. AU - Eilmes, K. J. AU - Grasemann, H. AU - Torres, B. AU - Knauer, N. AU - Sroka, K. AU - Insel, P. A. AU - Ratjen, F. PY - 2002 DA - 2002// TI - β2 adrenoceptor gene polymorphisms in cystic fibrosis lung disease JO - Pharmacogenet Genomics VL - 12 UR - https://doi.org/10.1097/00008571-200207000-00002 DO - 10.1097/00008571-200207000-00002 ID - Büscher2002 ER - TY - JOUR AU - Steagall, W. K. AU - Barrow, B. J. AU - Glasgow, C. G. AU - Mendoza, J. W. AU - Ehrmantraut, M. AU - Lin, J. -. P. AU - Insel, P. A. AU - Moss, J. PY - 2007 DA - 2007// TI - Beta-2-adrenergic receptor polymorphisms in cystic fibrosis JO - Pharmacogenet Genomics VL - 17 UR - https://doi.org/10.1097/FPC.0b013e3280119349 DO - 10.1097/FPC.0b013e3280119349 ID - Steagall2007 ER - TY - JOUR AU - Bristow, M. AU - Hershberger, R. AU - Port, J. AU - Gilbert, E. AU - Sandoval, A. AU - Rasmussen, R. AU - Cates, A. AU - Feldman, A. PY - 1990 DA - 1990// TI - Beta-adrenergic pathways in nonfailing and failing human ventricular myocardium JO - Circulation VL - 82 UR - https://doi.org/10.1161/01.CIR.82.2.658 DO - 10.1161/01.CIR.82.2.658 ID - Bristow1990 ER - TY - JOUR AU - Hull, J. H. AU - Ansley, L. AU - Bolton, C. E. AU - Sharman, J. E. AU - Knight, R. K. AU - Cockcroft, J. R. AU - Shale, D. J. AU - Garrod, R. PY - 2011 DA - 2011// TI - The effect of exercise on large artery haemodynamics in cystic fibrosis JO - J Cyst Fibros VL - 10 UR - https://doi.org/10.1016/j.jcf.2010.12.001 DO - 10.1016/j.jcf.2010.12.001 ID - Hull2011 ER - TY - JOUR AU - Snyder, E. M. AU - Wong, E. C. AU - Foxx‐Lupo, W. T. AU - Wheatley, C. M. AU - Cassuto, N. A. AU - Patanwala, A. E. PY - 2011 DA - 2011// TI - Effects of an Inhaled β2-Agonist on Cardiovascular Function and Sympathetic Activity in Healthy Subjects JO - Pharmacotherapy VL - 31 UR - https://doi.org/10.1592/phco.31.8.748 DO - 10.1592/phco.31.8.748 ID - Snyder2011 ER - TY - JOUR AU - Miller, M. R. AU - Hankinson, J. AU - Brusasco, V. AU - Burgos, F. AU - Casaburi, R. AU - Coates, A. AU - Crapo, R. AU - Enright, P. AU - Grinten, C. P. AU - Gustafsson, P. PY - 2005 DA - 2005// TI - Standardisation of spirometry JO - Eur Respir J VL - 26 UR - https://doi.org/10.1183/09031936.05.00034805 DO - 10.1183/09031936.05.00034805 ID - Miller2005 ER - TY - JOUR AU - Snyder, E. M. AU - Johnson, B. D. AU - Beck, K. C. PY - 2005 DA - 2005// TI - An open-circuit method for determining lung diffusing capacity during exercise: comparison to rebreathe JO - J Appl Physiol (1985) VL - 99 UR - https://doi.org/10.1152/japplphysiol.00348.2005 DO - 10.1152/japplphysiol.00348.2005 ID - Snyder2005 ER - TY - JOUR AU - Lang, C. C. AU - Karlin, P. AU - Haythe, J. AU - Lim, T. K. AU - Mancini, D. M. PY - 2009 DA - 2009// TI - Peak cardiac power output, measured noninvasively, is a powerful predictor of outcome in chronic heart failure JO - Circ Heart Fail VL - 2 UR - https://doi.org/10.1161/CIRCHEARTFAILURE.108.798611 DO - 10.1161/CIRCHEARTFAILURE.108.798611 ID - Lang2009 ER - TY - JOUR AU - Cotter, G. AU - Moshkovitz, Y. AU - Kaluski, E. AU - Milo, O. AU - Nobikov, Y. AU - Schneeweiss, A. AU - Krakover, R. AU - Vered, Z. PY - 2003 DA - 2003// TI - The role of cardiac power and systemic vascular resistance in the pathophysiology and diagnosis of patients with acute congestive heart failure JO - Eur J Heart Fail VL - 5 UR - https://doi.org/10.1016/S1388-9842(03)00100-4 DO - 10.1016/S1388-9842(03)00100-4 ID - Cotter2003 ER - TY - JOUR AU - Bromley, P. D. AU - Hodges, L. D. AU - Brodie, D. A. PY - 2006 DA - 2006// TI - Physiological range of peak cardiac power output in healthy adults JO - Clin Physiol Funct Imaging VL - 26 UR - https://doi.org/10.1111/j.1475-097X.2006.00678.x DO - 10.1111/j.1475-097X.2006.00678.x ID - Bromley2006 ER - TY - JOUR AU - Hansen, J. E. AU - Sue, D. Y. AU - Wasserman, K. PY - 1984 DA - 1984// TI - Predicted values for clinical exercise testing JO - Am Rev Respir Dis VL - 129 UR - https://doi.org/10.1164/arrd.1984.129.2P2.S49 DO - 10.1164/arrd.1984.129.2P2.S49 ID - Hansen1984 ER - TY - JOUR AU - Hsia, C. C. AU - Herazo, L. F. AU - Ramanathan, M. AU - Johnson, R. L. PY - 1995 DA - 1995// TI - Cardiac output during exercise measured by acetylene rebreathing, thermodilution, and Fick techniques JO - J Appl Physiol (1985) VL - 78 ID - Hsia1995 ER - TY - JOUR AU - Johnson, B. D. AU - Beck, K. C. AU - Proctor, D. N. AU - Miller, J. AU - Dietz, N. M. AU - Joyner, M. J. PY - 2000 DA - 2000// TI - Cardiac output during exercise by the open circuit acetylene washin method: comparison with direct Fick JO - J Appl Physiol (1985) VL - 88 ID - Johnson2000 ER - TY - JOUR AU - Nakagawa, S. AU - Cuthill, I. C. PY - 2007 DA - 2007// TI - Effect size, confidence interval and statistical significance: a practical guide for biologists JO - Biol Rev Camb Philos Soc VL - 82 UR - https://doi.org/10.1111/j.1469-185X.2007.00027.x DO - 10.1111/j.1469-185X.2007.00027.x ID - Nakagawa2007 ER - TY - JOUR AU - Lakens, D. PY - 2013 DA - 2013// TI - Calculating and reporting effect sizes to facilitate cumulative science: a practical primer for t-tests and ANOVAs JO - Front Psychol VL - 4 UR - https://doi.org/10.3389/fpsyg.2013.00863 DO - 10.3389/fpsyg.2013.00863 ID - Lakens2013 ER - TY - JOUR AU - Ichinose, M. J. AU - Sala-Mercado, J. A. AU - Coutsos, M. AU - Li, Z. AU - Ichinose, T. K. AU - Dawe, E. AU - O’Leary, D. S. PY - 2010 DA - 2010// TI - Modulation of cardiac output alters the mechanisms of the muscle metaboreflex pressor response JO - Am J Physiol Heart Circ Physiol VL - 298 UR - https://doi.org/10.1152/ajpheart.00909.2009 DO - 10.1152/ajpheart.00909.2009 ID - Ichinose2010 ER - TY - JOUR AU - Spranger, M. D. AU - Sala-Mercado, J. A. AU - Coutsos, M. AU - Kaur, J. AU - Stayer, D. AU - Augustyniak, R. A. AU - O’Leary, D. S. PY - 2013 DA - 2013// TI - Role of cardiac output versus peripheral vasoconstriction in mediating muscle metaboreflex pressor responses: dynamic exercise versus postexercise muscle ischemia JO - Am J Physiol Regul Integr Comp Physiol VL - 304 UR - https://doi.org/10.1152/ajpregu.00601.2012 DO - 10.1152/ajpregu.00601.2012 ID - Spranger2013 ER - TY - JOUR AU - Sellers, Z. M. AU - Kovacs, A. AU - Weinheimer, C. J. AU - Best, P. M. PY - 2013 DA - 2013// TI - Left ventricular and aortic dysfunction in cystic fibrosis mice JO - J Cyst Fibros VL - 12 UR - https://doi.org/10.1016/j.jcf.2012.11.012 DO - 10.1016/j.jcf.2012.11.012 ID - Sellers2013 ER - TY - JOUR AU - Sellers, Z. M. AU - Naren, A. P. AU - Xiang, Y. AU - Best, P. M. PY - 2012 DA - 2012// TI - MRP4 and CFTR in the regulation of cAMP and beta-adrenergic contraction in cardiac myocytes JO - Eur J Pharmacol VL - 681 UR - https://doi.org/10.1016/j.ejphar.2012.02.018 DO - 10.1016/j.ejphar.2012.02.018 ID - Sellers2012 ER - TY - JOUR AU - Duan, D. Y. AU - Liu, L. L. AU - Bozeat, N. AU - Huang, Z. M. AU - Xiang, S. Y. AU - Wang, G. L. AU - Ye, L. AU - Hume, J. R. PY - 2005 DA - 2005// TI - Functional role of anion channels in cardiac diseases JO - Acta Pharmacol Sin VL - 26 UR - https://doi.org/10.1111/j.1745-7254.2005.00061.x DO - 10.1111/j.1745-7254.2005.00061.x ID - Duan2005 ER - TY - JOUR AU - Naren, A. P. AU - Cobb, B. AU - Li, C. AU - Roy, K. AU - Nelson, D. AU - Heda, G. D. AU - Liao, J. AU - Kirk, K. L. AU - Sorscher, E. J. AU - Hanrahan, J. AU - Clancy, J. P. PY - 2003 DA - 2003// TI - A macromolecular complex of beta 2 adrenergic receptor, CFTR, and ezrin/radixin/moesin-binding phosphoprotein 50 is regulated by PKA JO - Proc Natl Acad Sci U S A VL - 100 UR - https://doi.org/10.1073/pnas.0135434100 DO - 10.1073/pnas.0135434100 ID - Naren2003 ER - TY - JOUR AU - Uezono, Y. AU - Bradley, J. AU - Min, C. AU - McCarty, N. AU - Quick, M. AU - Riordan, J. AU - Chavkin, C. AU - Zinn, K. AU - Lester, H. AU - Davidson, N. PY - 1992 DA - 1992// TI - Receptors that couple to 2 classes of G proteins increase cAMP and activate CFTR expressed in Xenopus oocytes JO - Receptors Channels VL - 1 ID - Uezono1992 ER - TY - STD TI - Taouil K, Hinnrasky J, Hologne C, Corlieu P, Klossek J-M, Puchelle E. Stimulation of β2 adrenergic receptor increases CFTR expression in human airway epithelial cells through a c-AMP/protein kinase A-independent pathway. J Biol Chem. 2003. ID - ref40 ER - TY - JOUR AU - McCann, J. D. AU - Bhalla, R. C. AU - Welsh, M. J. PY - 1989 DA - 1989// TI - Release of intracellular calcium by two different second messengers in airway epithelium JO - Am J Physiol VL - 257 ID - McCann1989 ER - TY - JOUR AU - Wheatley, C. M. AU - Wilkins, B. W. AU - Snyder, E. M. PY - 2011 DA - 2011// TI - Exercise is medicine in cystic fibrosis JO - Exerc Sport Sci Rev VL - 39 UR - https://doi.org/10.1097/JES.0b013e3182172a5a DO - 10.1097/JES.0b013e3182172a5a ID - Wheatley2011 ER - TY - JOUR AU - Davis, P. B. AU - Shelhamer, J. R. AU - Kaliner, M. PY - 1980 DA - 1980// TI - Abnormal adrenergic and cholinergic sensitivity in cystic fibrosis JO - N Engl J Med VL - 302 UR - https://doi.org/10.1056/NEJM198006263022605 DO - 10.1056/NEJM198006263022605 ID - Davis1980 ER - TY - JOUR AU - Xiao, R. P. AU - Lakatta, E. G. PY - 1993 DA - 1993// TI - Beta 1-adrenoceptor stimulation and beta 2-adrenoceptor stimulation differ in their effects on contraction, cytosolic Ca2+, and Ca2+ current in single rat ventricular cells JO - Circ Res VL - 73 UR - https://doi.org/10.1161/01.RES.73.2.286 DO - 10.1161/01.RES.73.2.286 ID - Xiao1993 ER - TY - JOUR AU - Altschuld, R. A. AU - Starling, R. C. AU - Hamlin, R. L. AU - Billman, G. E. AU - Hensley, J. AU - Castillo, L. AU - Fertel, R. H. AU - Hohl, C. M. AU - Robitaille, P. M. AU - Jones, L. R. PY - 1995 DA - 1995// TI - Response of failing canine and human heart cells to beta 2-adrenergic stimulation JO - Circulation VL - 92 UR - https://doi.org/10.1161/01.CIR.92.6.1612 DO - 10.1161/01.CIR.92.6.1612 ID - Altschuld1995 ER - TY - JOUR AU - Boutjdir, M. AU - Restivo, M. AU - Wei, Y. AU - el-Sherif, N. PY - 1992 DA - 1992// TI - Alpha 1- and beta-adrenergic interactions on L-type calcium current in cardiac myocytes JO - Pflugers Arch VL - 421 UR - https://doi.org/10.1007/BF00374231 DO - 10.1007/BF00374231 ID - Boutjdir1992 ER - TY - JOUR AU - Hool, L. C. AU - Arthur, P. G. PY - 2002 DA - 2002// TI - Decreasing cellular hydrogen peroxide with catalase mimics the effects of hypoxia on the sensitivity of the L-type Ca2+ channel to beta-adrenergic receptor stimulation in cardiac myocytes JO - Circ Res VL - 91 UR - https://doi.org/10.1161/01.RES.0000035528.00678.D5 DO - 10.1161/01.RES.0000035528.00678.D5 ID - Hool2002 ER - TY - JOUR AU - Newnham, D. AU - Wheeldon, N. AU - Lipworth, B. AU - McDevitt, D. PY - 1993 DA - 1993// TI - Single dosing comparison of the relative cardiac beta 1/beta 2 activity of inhaled fenoterol and salbutamol in normal subjects JO - Thorax VL - 48 UR - https://doi.org/10.1136/thx.48.6.656 DO - 10.1136/thx.48.6.656 ID - Newnham1993 ER - TY - JOUR AU - Vaisman, N. AU - Koren, G. AU - Goldstein, D. AU - Canny, G. J. AU - Tan, Y. AU - Soldin, S. AU - Pencharz, P. PY - 1987 DA - 1987// TI - Pharmacokinetics of inhaled salbutamol in patients with cystic fibrosis versus healthy young adults JO - J Pediatr VL - 111 UR - https://doi.org/10.1016/S0022-3476(87)80218-4 DO - 10.1016/S0022-3476(87)80218-4 ID - Vaisman1987 ER -