From: Decreased systemic bioavailability of L-arginine in patients with cystic fibrosis
CF patients (n = 10) | ||||
---|---|---|---|---|
Controls (n = 10) | before (% control) | after (% control) | P-value | |
L-arginine | 67.7 ± 19.0 | 48.1 ± 19.9 (71) * | 68.9 ± 19.5 (102) | 0.02 |
L-ornithine | 45.7 ± 13.8 | 56.6 ± 34.0 (124) | 65.9 ± 15.5 (144)† | NS |
L-citrulline | 27.5 ± 8.8 | 28.3 ± 5.5 (103) | 33.4 ± 5.8 (121) | NS |
Threonine | 128.1 ± 40.0 | 87.2 ± 30.7 (68) * | 129.7 ± 50.4 (101) | 0.01 |
Serine | 97.7 ± 30.0 | 92.0 ± 26.3 (94) | 92.9 ± 17.2 (95) | NS |
Asparagine | 52.5 ± 14.5 | 37.3 ± 12.4 (71) * | 40.0 ± 11.0 (76) | NS |
Glutamic Acid | 18.6 ± 7.1 | 69.7 ± 40.7 (375) † | 65.7 ± 52.5 (353)* | NS |
Proline | 170.3 ± 31.8 | 165.4 ± 43.2 (97) | 216.8 ± 57.5 (127)* | NS |
Glycine | 205.1 ± 52.9 | 241.8 ± 100.6 (118) | 323.5 ± 69.1 (158)† | 0.02 |
Alanine | 328.5 ± 73.6 | 243.1 ± 90.8 (74) * | 355.3 ± 139.6 (108) | NS |
Valine | 203.0 ± 25.0 | 169.7 ± 32.1 (84) * | 176.1 ± 39.6 (87) | NS |
Cysteine | 55.3 ± 15.6 | 30.1 ± 9.0 (54) † | 42.4 ± 13.7 (77) | 0.004 |
Methionine | 24.9 ± 4.8 | 19.2 ± 5.2 (77) * | 21.0 ± 5.6 (84) | NS |
Isoleucine | 57.6 ± 10.9 | 52.3 ± 18.1 (91) | 62.9 ± 12.9 (109) | NS |
Leucine | 111.3 ± 22.2 | 90.4 ± 25.1 (81) | 96.1 ± 23.9 (86) | NS |
Tyrosine | 54.7 ± 9.8 | 45.7 ± 14.3 (84) | 44.7 ± 11.3 (82) | NS |
Phenylalanine | 49.9 ± 6.8 | 47.7 ± 10.7 (96) | 49.0 ± 10.3 (98) | NS |
Histidine | 83.7 ± 7.2 | 55.9 ± 17.7 (67) † | 64.4 ± 17.6 (77)† | NS |
Tryptophan | 49.8 ± 9.5 | 30.7 ± 15.8 (62) † | 46.6 ± 11.7 (94) | 0.02 |
Lysine | 144.7 ± 42.5 | 144.0 ± 40.5 (100) | 183.8 ± 51.9 (127) | NS |