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Table 1 Clinical characteristics of cystic fibrosis patients.

From: Peroxisome Proliferator-Activated Receptor α (PPARα) down-regulation in cystic fibrosis lymphocytes

Patient

Age (years)

Gender

Genotype

P.a.1

CRP

FEV1 % pred2

FVC % pred2

1

33

F

dF508/R553x

+

0,9

58

91

2

25

M

dF508/dF508

+

0,5

74

90

3

30

M

dF508/dF508

+

0,7

42

72

4

34

M

dF508/?

+

0,3

59

80

5

37

M

dF508/dF508

+

0,6

52

84

6

32

F

dF508/dF508

+

2

60

75

7

26

F

dF508/dF508

+

1,32

86

87

8

28

M

dF508/?

+

0,91

31

48

9

37

M

dF508/dF508

+

< 0,3

30

43

10

32

F

dF508/dF508

+

< 0,3

76

92

11

23

M

dF508/?

+

< 0,3

103

99

12

37

M

dF508/dF508

-

< 0,3

74

101

13

34

F

dF508/dF508

+

0,94

23

59

14

39

M

dF508/dF508

-

< 0,3

60

83

15

25

M

dF508/R553x

+

1,03

85,9

79,7

16

22

F

dF508/N1303

+

0,9

53,6

64,6

17

43

M

dF508/dF508

+

< 0,3

98,8

95,5

18

23

M

dF508/dF508

+

0,8

85,3

84,5

19

39

M

dF508/G542x

+

0,4

61

79

20

40

M

dF508/?

+

0,4

64

80

  1. 1Pseudomonas aeruginosa infection
  2. 2 Normal: 80–120% of predicted