From: A role for MCP-1/CCR2 in interstitial lung disease in children
No | Sex | Age [years] | Interstitial lung disease | Diagnosis finding | Radiographic findings | Fibrotic changes (CT) | ILD Score* | Dyspnoe | Cough | Cyanosis | Exercise Intolerance | Failure to thrive | Medication | FVC [% of pred.] | TLC % [of pred.] |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
1 | F | 7 | LIP | CT, LB | • diffuse interstitial involvement | + | 4 | ++ | + | + | + | + | CS, AZT | 34 | 56 |
 |  |  |  |  | • reticular-nodular pattern |  |  |  |  |  |  |  |  |  |  |
 |  |  |  |  | • follicular bronchiolitis |  |  |  |  |  |  |  |  |  |  |
2 | M | 14 | U-ILD, IPH | CT, BAL | patchy interstitial involvement | - | 2 | + | - | - | - | - | CS | 77 | 89 |
3 | M | 8 | U-ILD | CT, LB | • ground-glass opacity | + | 3 | ++ | - | - | + | - |  | 46 | 74 |
4 | M | 4 | IPH | CT, BAL, LB | interstitial involvement | - | 3 | + | - | - | - | - | Â | 77 | 168 |
5 | M | 16 | U-ILD | CT, BAL | interstitial involvement | + | 2 | + | - | - | + | + | Â | 76 | 95 |
6 | F | 7 | U-ILD | CT, BAL | interstitial involvement | - | 2 | + | + | - | - | + | AZT | 50 | 68 |
7 | M | 4 | CPI | CT, LB | • diffuse infiltrates | + | 3 | + | - | - | + | + | AZT | 58 | 64 |
 |  |  |  |  | • ground-glass opacity |  |  |  |  |  |  |  |  |  |  |
8 | F | 3 | NSIP | CT, LB | • interstitial involvement | + | 3 | ++ | - | + | + | + | CS | n.d. | n.d. |
 |  |  |  |  | • alveolar infiltrates |  |  |  |  |  |  |  |  |  |  |
9 | M | 8 | Sarcoidosis | CT, BAL, LB | • interstitial involvement | + | 2 | ++ | + | - | + | + | CS | 56 | 63 |
 |  |  |  |  | • perivascular nodules |  |  |  |  |  |  |  |  |  |  |
10 | F | 8 | U-ILD | CT, BAL, LB | ground-glass opacity | - | 1 | - | + | - | + | - | Â | 76 | 87 |
11 | F | 8 | CPI | CT, LB | • interstitial involvement | + | 2 | + | + | - | + | + | CS | 37 | 74 |
 |  |  |  |  | • ground-glass opacity |  |  |  |  |  |  |  |  |  |  |
12 | M | 9 | U-ILD | CT | interstitial involvement | - | 2 | + | - | - | - | - | Â | 70 | 98 |
13 | M | 5 | NSIP | CT, LB | • interstitial involvement | + | 3 | ++ | - | - | + | - | CS | 61 | 76 |
 |  |  |  |  | • ground-glass opacity |  |  |  |  |  |  |  |  |  |  |
14 | F | 6 | U-ILD | CT | reticular-nodular pattern | + | 3 | ++ | + | - | - | - | AZT | 60 | 68 |
15 | F | 4 | U-ILD | CT | interstitial involvement | + | 2 | + | + | - | - | + | Â | n.d. | n.d. |
16 | M | 12 | U-ILD | CT | interstitial involvement | - | 2 | + | - | - | - | - | Â | 68 | 75 |
17 | M | 3 | PAP†| CT, BAL, LB | • ground glass opacity | - | 4 | +++ | + | + | + | + | CS | n.d. | n.d. |
18 | M | 6 | NSIP | CT, BAL, LB | • alveolar infiltrates | + | 4 | +++ | + | + | + | + | CS, AZT | 63 | 72 |
 |  |  | PAP |  | • ground glass opacification |  |  |  |  |  |  |  |  |  |  |
19 | F | 3 | PAP†| CT, BAL, LB | • ground glass opacity | + | 4 | ++ | - | + | + | + | CS | n.d. | n.d. |
 |  |  |  |  | • alveolar infiltrates |  |  |  |  |  |  |  |  |  |  |
20 | F | 9 | NSIP | CT, LB | • interstitial involvement | + | 3 | ++ | + | + | + | + | CS, AZT | 55 | 74 |
 |  |  |  |  | • honeycombing |  |  |  |  |  |  |  |  |  |  |
21 | M | 7 | U-ILD | CT | reticular-interstitial pattern | + | 3 | + | + | - | + | + | AZT, MT | 38 | 59 |
22 | M | 7 | Cholesterol | CT, BAL, LB | • interstitial involvement | + | 4 | +++ | + | + | + | + | CS | 16 | 24 |
 |  |  | pneumonitis†|  | • reticular-interstitial pattern |  |  |  |  |  |  |  |  |  |  |
23 | M | 4 | U-ILD | CT, LB | • interstitial involvement | - | 2 | + | - | - | + | + | CS | 102 | 99 |
 |  |  |  |  | • honeycombing |  |  |  |  |  |  |  |  |  |  |
24 | M | 8 | U-ILD | CT | interstitial involvement | - | 2 | + | + | - | + | - | CS | 63 | 78 |
25 | M | 7 | NSIP | CT, LB | • interstitial involvement | + | 3 | + | + | - | + | - | CS | 60 | 76 |