Patients | Sex | Body weight | age at diagnosis | age at follow up | number of lavage sessions | number of 500 ml portions per lavage | total lavage volume recovered per lung | volume/b.w | ||
---|---|---|---|---|---|---|---|---|---|---|
(kg) | (y) | (y) | left | right | left lung | right lung | (ml) | (ml/kg) | ||
PAP ped. (J01) | m | 8.5 | 1.75 | 5.8 | 9 | 11 | 9 (6.5/10) | 6 (4/7) | 3258 (2780/4080) | 383.3 |
PAP ped. (J02) | f | 14.5 | 1.75 | 7.8 | 6 | 6 | 7.5 (5.5/10) | 7 (5.5/9.5) | 3353 (2862/3913) | 231.2 |
PAP ped. (J03) | f | 4.5 | 0.33 | died at age 1/3 | 1 | 1 | 2 | 8 | 270.3 | 60.1 |
PAP ped. (J04) | m | 4.3 | 0.08 | died at age 1/4 | 1 | 1 | 2 | 4 | 1018.3 | 236.8 |
median (25/75 percentile) | 6.5 (4.4/11.5)++ | 1.0 (0.2/2.3)++ | 2007 (644.3/3199) | 234 (145.7/310) | ||||||
PAP adult (A01) | f | 70.0 | 39.5 | alive | 1 | 1 | 28 | 29 | 14102 | 201.5 |
PAP adult (A02) | f | 69.6 | 39 | alive | 1 | 0 | 13 | 0 | 6608 | 94.4 |
PAP adult (A03) | f | 69.7 | 49 | alive | 0 | 1 | 0 | 35 | 17659 | 252.3 |
PAP adult (A04) | f | 70.2 | 37 | alive | 0 | 1 | 0 | 27 | 27000 | 385.7 |
PAP adult (A05)# | m | 80.5 | 51.5 | alive | 1 | 1 | 20 | 24 | 22000 | 275 |
PAP adult (A06)# | m | 80.1 | 43.5 | alive | 1 | 1 | 31 | 39 | 35000 | 437.5 |
median (25/75 percentile) | 70.1 (69.7/80.3) | 42 (38/50) | 19830 (10355/31000)$$ | 263.7 (248/411.6)$ | ||||||
Cholesterol – Pneumonitis (L01) | m | 13 | 6.5 | 13.5. LTX | 1 | 1 | n.a. | 2 | 577.5 | 44.4 |
control (C01) | f | 13 | 1.5 | n.a. | 0 | 1 | n.a. | n.a. | 12 | 0.9 |
control (C02) | m | 20 | 5 | n.a. | 0 | 1 | n.a. | n.a. | 48 | 2.4 |
control (C03) | m | 16 | 4 | n.a. | 0 | 1 | n.a. | n.a. | 23 | 1.4 |
control (C04) | m | 11 | 3 | n.a. | 0 | 1 | n.a. | n.a. | 17 | 1.6 |
control (C05) | f | 11 | 2.5 | n.a. | 0 | 1 | n.a. | n.a. | 21 | 1.9 |
control (C06) | m | 8.5 | 1.5 | n.a. | 1 | 0 | n.a. | n.a. | 21 | 2.5 |
control (C07) | f | 7 | 0.5 | n.a. | 1 | 0 | n.a. | n.a. | 12.5 | 1.8 |
control (C08) | m | 10 | 1.5 | n.a. | 1 | 0 | n.a. | n.a. | 14 | 1.4 |
control (C09) | m | 11 | 2 | n.a. | 1 | 0 | n.a. | n.a. | 17 | 1.6 |
control (C10) | m | 36 | 10.5 | n.a. | 1 | 0 | n.a. | n.a. | 65 | 1.8 |
median (25/75 percentile) | 11 (9.3/18) | 2.3 (1.5/4.5) | 19 (13.3/35) | 1.7 (1.4/2.2) |