Etiology of PAH n(%) | Ā |
---|---|
Idiopathic | 21(75%) |
Heritable | 3(10.7%) |
Drug and toxin-induced | 1(3.6%) |
Associated with | 3(10.7%) |
NYHA class n(%) | Ā |
I | 4(14%) |
II | 14(50%) |
III | 10(36%) |
IV | 0(0%) |
Medications n(%) | Ā |
Prostacyclin | 6(21.4%) |
PDE5i | 4(14.3%) |
ERA | 4(14.3%) |
Prostacyclinā+āPDE5i | 4(14.3%) |
Prsoatcyclinā+āERA | 2(7.15%) |
ERAā+āPDE5i | 2(7.15%) |
Prostacyclinā+āPDE5iā+āERA | 6(21.4%) |
6-MWD (m) | 487Ā±24 |
Right ventricular systolic pressure (mmHg) | 78 Ā±5 |
Mean pulmonary arterial pressure (mmHg) | 52Ā±3 |
Mean pulmonary capillary wedge pressure (mmHg) | 13Ā±1 |
Cardiac output (L/min) | 6Ā±0.4 |
Cardiac index (L/min/m2) | 3Ā±0.2 |
Pulmonary vascular resistance (wood units) | 7.8Ā±0.9 |