Table 1 Summary of the ERS guidelines for the diagnosis of LAM

Definite LAM

1. Characteristic or compatible lung HRCT AND lung biopsy fitting the pathological criteria for LAM OR

2. Characteristic lung HRCT and any of the following:

· Angiomyolipoma (kidney)

· Thoracic or abdominal chylous effusion

· Lymphangioleiomyoma or lymph node involvement by LAM

· Definite or probable TSC

Probable LAM

1. Characteristic HRCT and compatible clinical history OR

2. Compatible HRCT and any of the following:

· Angiomyolipoma (kidney)

· Thoracic or abdominal chylous effusion

Possible LAM

Characteristic or compatible HRCT