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Table 2 Further definition of the underlying NCFB etiologies

From: Risk factors for morbidity and death in non-cystic fibrosis bronchiectasis: a retrospective cross-sectional analysis of CT diagnosed bronchiectatic patients

Postinfectious (84)

TB (37), MAC (5), Pertussis (3), Invasive Aspergillosis (2), Measles (1), Diphtheria (1), Blastocystes hominis (1), unkown (34)

COPD (64)

GOLD II (10), GOLD III (28), GOLD IV (26)

Interstitial lung disease (57)

EAA (15), IPF/NSIP (27), BOOP (9), drug induced ILD (3), UIP (3)

Rheumatic lung disease RA (29), Sjögren (5), Sclerodermia (4), AS (1), MCTD (1) (40)

Immunodeficiency (29)

CVID (1), HIV (1), hyper IgE syndrome (1), other immunoglobulin deficits (14 dysgammaglobulinemia, 1 agammaglobulinemia, 2 hypogamma-globulinemia), Navajo poikiloderma (1), different types of post transplants (5) (3 kidney, 1 liver and 1 heart), non-thoracic Non-Hodgkin lymphoma (2), chronic lymphatic leukemia (1)

Thoracic cancer (38)

adenocarcinoma (9), large cell anaplastic carcinoma (1), squamous cell carcinoma (16), small-cell lung carcinoma (3), thoracic Non-Hodgkin lymphoma (3), carcinoid (1), mesothelioma (2), solitary pulmonary nodule without tissue diagnosis (3)

Other causes (44)

sarcoidosis (13), anatomic malformations (6), UC (6), Crohn (3), SJM (3), aspiration/inhalation (3), α1-ATD (2), CS vasculitis (2), Wegener (2), MK (1), PE (1), WC (1), Microscopic polyangiitis (1)

  1. The number in brackets states the number of patients. AS = Ankylosing Spondylitis, α 1 -ATD = alfa-1-antitrypsin deficiency, BOOP = Bronchiolitis Obliterans Organizing Pneumonia, COPD = Chronic Obstructive Lung Disease, CS = Churg-Strauss, CVID = Common Variable Immunodeficiency, EAA = Extrinsic Allergic Alveolitis, ILD = Interstitial Lung Disease, IPF = Idiopathic Pulmonary Fibrosis, MAC = Mycobacterium avium complex, MCTD = Mixed Connective Tissue Disease, MK = Mounier-Kuhn Syndrome, NSIP = Nonspecific Interstitial Pneumonia, PE = Pseudoxanthoma Elasticum, RA = Rheumatoid Arthritis, SJM = Swyer-James-McLeod Syndrome, TB = Tuberculosis, UC = Ulcerative Colitis, UIP = Usual Interstitial Pneumonia, WC = Williams-Campbell syndrome